Síndrome de Laugier-Hunziker / Laugier-hunziker syndrome

Rodrigo Guerra Sabongi, Natalia Petri Dias, Julia Rezende Duek, Vânia Penha Guerra Sabongi

Resumo


A síndrome de Laugier-Hunziker é uma desordem adquirida rara, benigna, de etiopatogenia desconhecida, inicialmente descrita em 1970, caracterizada por hiperpigmentação macular mucocutânea frequentemente associada à melanoníquia longitudinal. O diagnóstico é clínico, excluindo outras causas de hiperpigmentação mucocutânea, podendo a dermatoscopia correlacionar-se com os achados histológicos da síndrome. Relatamos um caso de Síndrome de Laugier-Hunziker, com base em seus achados clínicos e dermatoscópicos.
Descritores: hiperpigmentação, syndrome, dermoscopia, lentigo.

ABSTRACT
Laugier-Hunziker syndrome is a rare benign acquired disorder of unknown pathogenesis, firstly described in 1970, characterized by macular mucocutaneous hyperpigmentation frequently associated with longitudinal melanonychia. Diagnosis is essentially clinical, therefore other causes of mucocutaneous hyperpigmentation in which dermatoscopy can correlate with histological findings of the syndrome must be excluded. We report a case of Laugier-Hunziker syndrome based on clinical and dermatoscopic findings.
Key-words: hyperpigmentation, syndrome, dermocospy, lentigo.

Palavras-chave


hiperpigmentação; syndrome; dermoscopia; lentigo

Referências


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