Granulomatose com poliangiite: relato de caso

Beatriz Castro Ribeiro; Cibele Isaac Saad Rodrigues; Ronaldo D'Avila

doi:10.23925/1984-4840.2018v20i4a9

Authors

Beatriz Castro Ribeiro Pontifícia Universidade Católica de São Paulo (PUC-SP), Faculdade de Ciências Médicas de Sorocaba (FCMS) – Sorocaba (SP), Brasil. http://orcid.org/0000-0002-0706-2090
Cibele Isaac Saad Rodrigues Pontifícia Universidade Católica de São Paulo (PUC-SP), Faculdade de Ciências Médicas de Sorocaba (FCMS) – Sorocaba (SP), Brasil. http://orcid.org/0000-0001-9490-7997
Ronaldo D'Avila Pontifícia Universidade Católica de São Paulo (PUC-SP), Faculdade de Ciências Médicas de Sorocaba (FCMS) – Sorocaba (SP), Brasil. http://orcid.org/0000-0001-5422-9650

DOI:

https://doi.org/10.23925/1984-4840.2018v20i4a9

Keywords:

granulomatosis with polyangiitis, vasculitis, vascular diseases, autoimmune diseases, respiratory tract diseases

Abstract

Granulomatosis with polyangiitis (GPA), previously called Wegener’s granulomatosis, is a systemic granulomatous necrotizing vasculitis, pauci-immune, which predominantly affects the upper respiratory tract, lungs and kidneys. Patients affected by this disease may have general and specific symptoms of upper or pulmonary, kidney, cutaneous or another organ involvement. The treatment is mainly carried out with immunosuppressive drugs and should be instituted as early as possible. This report describes the clinical and laboratory characteristics and the evolution of patients with GPA in outpatient follow-up.

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Author Biographies

Beatriz Castro Ribeiro, Pontifícia Universidade Católica de São Paulo (PUC-SP), Faculdade de Ciências Médicas de Sorocaba (FCMS) – Sorocaba (SP), Brasil.

Estudante de graduação em Medicina na Faculdade de Ciências Médicas e da Saúde, campus Sorocaba - PUC-SP

Cibele Isaac Saad Rodrigues, Pontifícia Universidade Católica de São Paulo (PUC-SP), Faculdade de Ciências Médicas de Sorocaba (FCMS) – Sorocaba (SP), Brasil.

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